Idiopathic Linear Calcinosis Cutis - A Case Report
Abstract
Linear calcinosis cutis is a very rare disorder; reported in association with lichen sclerosus atrophicus, scleroderma, after intravenous infusion of calcium and acute monocytic leukemia. In available literature idiopathic Zosteriform Calcinosis Cutis is yet to be described. Eight year old child presented with spontaneous painful, slowly progressive, linear band like nodules over right half of the chest and back of trunk. It is a rare presentation in Skin Department. On the basis of clinical, laboratory investigation and histopathology a diagnosis of Linear Calcinosis Cutis was made. So it was decided to report this rare case of idiopathic Zosteriform Calcinosis Cutis because of unusual presentation and rarity of the disorder.
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Introduction
Calcinosis cutis is an uncommon disorder, characterized by tender, hard skin coloured dermal nodules. Four distinct categories described; dystrophic, metastatic, iatrogenic and idiopathic. Morphological variants include nodular, plaque, tumoral and linear; occurring localized or generalized in distribution.1
Linear calcinosis cutis is a very rare entity; reported in association with (lichen sclerosus atrphicus) LSA, scleroderma, after intravenous infusion of calcium and acute monocytic leukemia.2,3,4,5,6
This zosteriform calcinosis cutis is described in association with LSA. In best of our knowledge idiopathic Zosteriform Calcinosis Cutis is yet to be described. It is a rare presentation in Skin Department. So it was decided to report this rare case of idiopathic Zosteriform Calcinosis Cutis because of unusual presentation and rarity of the disorder.
Conclusion
This case was idiopathic Zosteriform Calcinosis Cutis which is a rarely reported entity.